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A case of fibrillary glomerulonephritis with unusual IgM deposits and hypocomplementemia

Title
A case of fibrillary glomerulonephritis with unusual IgM deposits and hypocomplementemia
Authors
Shim Y.H.Lee S.J.Sung S.H.
Ewha Authors
이승주성순희
SCOPUS Author ID
이승주scopusscopus; 성순희scopus
Issue Date
2008
Journal Title
Pediatric Nephrology
ISSN
0931-041XJCR Link
Citation
Pediatric Nephrology vol. 23, no. 7, pp. 1163 - 1166
Indexed
SCIE; SCOPUS WOS scopus
Document Type
Article
Abstract
Fibrillary glomerulonephritis (FGN) is rare immune-mediated GN with predominant immunoglobulin (Ig) G deposits, normal serum complement levels, and poor prognosis. The incidence of FGN is less than 1% in the adult population, and only six pediatric cases have been reported in the English literature. A 12-year-old girl presented with acute nephrotic-nephritic syndrome mimicking atypical clinical features of acute poststreptococcal GN (APSGN). Clinical features had completely resolved in 2 weeks, but the serum complement levels remained low. Renal biopsy was done 6 months later, and she was diagnosed as having FGN with unusual IgM deposits. Despite persistently low serum complement levels during the subsequent 3 years, clinical relapse did not develop. This case was an atypical form of FGN characterized by unusual IgM deposits, persistent hypocomplementemia, and good prognosis, which suggests that childhood FGN is not necessarily a disease with poor prognosis. © IPNA 2008.
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DOI
10.1007/s00467-008-0765-6
Appears in Collections:
의과대학 > 의학과 > Journal papers
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